Somatosensory Conduction Pathway in Spastic Paraplegia Type 5
نویسندگان
چکیده
منابع مشابه
Somatosensory Conduction Pathway in Spastic Paraplegia Type 5
We describe herein the case of a 37-year-old woman who presented with slowly progressive lower-limb stiffness and gait ataxia. She complained of running difficulties since the age of 10 years, gait impairment since the age of 30 years, and uri-nary urgency during the past 2 years. Her family history was unremarkable. At the last examination she exhibited spastic gait, pyramidal signs, severe im...
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Cervical somatosensory evoked potentials elicited by median nerve stimulation were recorded from 18 cases of hereditary spastic paraplegia. Motor and sensory nerve conduction in the median nerve was normal in each. In one third of the patients no spinal evoked potential was detectable. In the remainder the amplitude of the evoked potential was reduced in comparison with a control series; the la...
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Central motor conduction (CMC) studies were carried out in 25 patients with hereditary spastic paraplegia (HSP). Responses evoked in the lower limbs by transcranial magnetic stimulation of the motor cortex were bilaterally absent in 33% of the patients and, when recordable, were delayed in 75% of cases. Responses in the upper limbs were mostly normal except for those from the five members of on...
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Hereditary spastic paraplegia (HSP) or Strümpell-Lorrain syndrome is a heterogeneous group of inherited disorders, with prevalence ranged from 4.3 to 9.6 cases per 100,000 population. A common feature of these disorders is the slowly progressive and often severe spasticity, noticeably especially in the low limbs. Conventionally, HSP is divided into two clinical groups, uncomplicated (pure spast...
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ژورنال
عنوان ژورنال: Journal of Clinical Neurology
سال: 2014
ISSN: 1738-6586,2005-5013
DOI: 10.3988/jcn.2014.10.4.373